// Classification of AML and MDS

CLASSIFICATION OF ACUTE LEUKEMIAS and MYELODYSPLASTIC SYNDROMES

Acute myeloid leukemias

Acute myeloid leukemia, minimally differentiated (MO).

Acute myeloid leukemia without maturation (M1).

Acute myeloid leukemia with maturation (M2).

Acute myeloid leukemia with maturation with t(8;21)

Acute promyelocytic leukemia (M3)

Hypergranular type Microgranular type

Acute myelomonocytic leukemia (M4)

Acute myelomonocytic leukemia with increased marrow eosinophils (M4EO)

Acute Monocytic Leukemia (M5)

Acute monoblastic leukemia (M5a)

Acute monocytic leukemia with maturation (M5b)

ErythroleukemiaErythroid /myeloid) (M6a)

Pure erythroid malignancy (M6b)

Acute megakaryoblastic leukemia (M7)

Acute megakaryoblastic leukemia associated with t(l;22)

Acute basophilic leukemiaAcute myelofibrosis (acute myelodysplasia with myelofibrosis)

Acute leukemia and transient myeloproliferative disorder in Down’s Syndrome

Hypocellular acute myeloid leukemiaMyeloid sarcoma

Acute lymphoblastic leukemias

Acute lymphoblastic leukemia (L1/L2)

Precursor B cell “Precursor” T cell Acute lymphoblastic leukemia, B-cell (L3) (equivalent to Burkitt Iymphoma in leukemic phase to be discussed with Burkitt Iymphoma)

Lymphoblastic lymphoma/leukemia

Precursor B-cell “Precursor” T-cellAcute leukemia, biphenotypic

MYELODYSPLASTIC SYNDROMES

Primary:

Refractory anemia

Refractory cytopenia with multilineage dysplasia

Refractory anemia with ringed sideroblasts

Refractory anemia with excess blasts

Refractory anemia with excess blasts in transformation

Chronic myelomonocytic leukemia

Chronic myelomonocytic leukemia in transformation

Therapy related:

Alkylating agent related

Epipodophyllotoxin related

CHRONIC MYELOPROLIFERATIVE DISORDERS

Chronic granulocytic leukemia

Atypical myeloproliferative syndrome (Ph-/BCR- myeloid leukemia)

Chronic myelomonocytic leukemia, myeloproliferative type

Chronic neutrophilic leukemiaHypereosinphilic syndrome

Chronic eosinophilic leukemia

Polycythemia vera

Essential thrombocythemia

Chronic idiopathic myelofibrosis with myeloid metaplasia

Chronic myeloproliferative syndrome, unclassifiableSystemic mastocytosis

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